Macrodystrophia lipomatosa with ulnar distribution in hand
نویسندگان
چکیده
منابع مشابه
Invasive macrodystrophia lipomatosa of the hand.
OBJECTIVE The Authors point out the interest of differential diagnosis and conservative surgical treatment of a rare case of digital and ulnar side of the hand gigantism, with massive fatty infiltration of soft tissues and a neurovascular bundle, to be included into Macrodystrophia Lipomatosa with fibrolipomatous hamartomata. PATIENTS AND METHODS Excision of the mass included 4th ray disartic...
متن کاملMacrodystrophia Lipomatosa
remaining three ulnar digits appeared normal. Magnetic resonance imaging (MRI) revealed characteristics of macrodystrophia lipomatosa such as enlargement and marked proliferation of the adipose tissues of the left hand, especially the radial aspect. MRI also demonstrated excessive fibrofatty tissue around the affected digits. This tissue has the same signal characteristics as fat on MRI, that i...
متن کاملMacrodystrophia lipomatosa: four case reports
AIM Macrodystrophia lipomatosa is a rare cause of gigantism of limb which can be confused with other common causes like congenital lymphedema. It presents usually with loss of function and cosmetic problems. Four cases are described with emphasis on clinical presentation, differential diagnoses, imaging and treatment options. METHODS & RESULTS Four patients of macrodystrophia lipomatosa were ...
متن کاملMR imaging of macrodystrophia lipomatosa.
Macrodystrophia lipomatosa is a rare nonhereditary congenital form of localised gigantism usually involving the 2nd or 3rd digit of the hand or foot. Pathologically an increase in adipose tissue involving subcutaneous tissue periosteum and bone marrow is present. Typical clinical andradiological appearances are described in this case report. Case Report A 36-year-old female presented with enlar...
متن کاملMacrodystrophia Lipomatosa: A rare presentation
Macrodystrophia lipomatosa is a rare congenital nonhereditary mesenchymal hamartomatous malformation resulting in localized gigantism of parts of extremities that manifests clinically as macrodactyly or megalodactyly. Radiological and Pathological hallmark is the disproportionate fibroadipose tissue proliferation in subcutaneous tissue, nerve sheaths, and periosteum that leads to soft tissue an...
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ژورنال
عنوان ژورنال: Journal of the Belgian Society of Radiology
سال: 2015
ISSN: 1780-2393
DOI: 10.5334/jbr-btr.753